Skip to main content

California Pizza hits KC and HPS in India

This evening I went out to eat with some great friends: Tina J, Tina B., Echo and Karen. We went to the California Pizza Company, which if you’ve never been, is GREAT! For all I know they’ve been open on the Plaza for a while, but I haven’t been to the Plaza in a while. It’s the same chain where we celebrated my being accepted into the drug trial back in August. (A shout out to the Washington HPS crew and Donna Rose!)

The menu has a little bit of everything from Southwestern to Asian influenced cuisine. It was also really nice to get out of the house. Last night I tried to go to Homers and escape for a bit – but when I got there the band was really rocking! Perhaps a little too rocking….am I getting old or something? I still need my eardrums, thank you very much. So, I got my weekly treat – a chai latte, and came home.

This weekend has been HPS weekend. I’ve already been working on the next newsletter, a few special requests from HPS’ers and I was doing some of my journal reviewing. Housework, what housework?

I’ve been so worried about Katy that I decided to take another pass at the journal searching. This time instead of searching for HPS I did searches about albinism.

We now have several families with adopted children from India that have tested positive for HPS – and I was really getting curious about another genetic founders effect. So, I got out a map and plotted where all the HPS’ers of Indian background came from. I didn’t find a connection. They were spread out all over India – and given that India is such a large and populous country, it stands to reason they’d have a number of HPS cases.

Then I had a brilliant idea (which should have occurred to me before today.) English is widely spoken in India and it may be likely Indian medical journals would be published in English. So, I went to Google Scholar Search (An excellent tool for doing medical journal searches by the way) and put in my request. Sure enough there are a number of researchers studying albinism in India. It turns out albinism is one of the leading causes of low vision in India, although I didn’t find any estimates of its frequency.

There was one paper that found a variant of OCA1 was quite common among the Tili ethnic group (hope I spelled that right.) I did find a few docs I will probably e-mail during the next few weeks just to find out if these gene hunters have even looked for Hermansky-Pudlak Syndrome in the populations they are studying. But, I didn’t find anything that might shed any light on Katy’s situation.

I did find one doc in Hyderbad that e-mailed me back within minutes of sending something off to him. He’s an ophthalmologist, but he says he had one patient he suspected might have HPS when he was a medical student. He wanted to discuss the issue further, but was not in his office – so we’re supposed to exchange more e-mails later this week.

Today I spent working on things for work. We’re starting to get near our deadline and I’m getting anxious about finishing everything – so I decided I’d sleep better this week and be less stressed if I got some headway made on my various projects. Yes, I think I could finish them within the week without working on Sunday – but I’d rather be ahead and have some flexibility to my schedule than be in a panic at the end of the week.

The really frustrating thing is that I didn’t make any headway on my personal stuff – like housework – and I’ve still got a pile of HPS things to do.

Comments

Popular posts from this blog

Ratner's Cheesecake

Here's another recipe from Toby! Thanks Toby......and I'll get the others posted soon! Ratner's Cheesecake and plain cookies Ratner's was a Jewish dairy restaurant in the lower East Side of Manhattan. This recipe, from my disintegrating, no longer in print Ratner's cookbook, is the closest I've ever gotten to reproducing the rich, heavy cheesecake my mother made when I was a kid. It's worth the time it takes to prepare and every last calorie. Dough Can be prepared in advance. Makes enough for two cakes. Can be frozen or used to make cookies – see recipe below. 1 cup sugar 1 teaspoon vanilla extract 1 cup shortening 1 teaspoon lemon extract 1 cup butter 2 eggs 3 cups sifted cake flour ½ teaspoon salt 2 cups all purpose flour 1 teaspoon baking powder 1. In a bowl, combine all ingredients with hands. Refrigerate 3 -4 hours, or preferably overnight. Filling (for

The next generation with Hermansky-Pudlak Syndrome

I'm so behind on posting about the trip to Puerto Rico. Since the episode of Mystery Diagnosis on Hermansky-Pudlak Syndrome ran right after we got home, it's been a little busy. These, however, are my favorite pictures from Puerto Rico. I know, not pretty senery etc - but these little guys and gals inspire me. They are the next generation of folks with HPS, and if we keep up the hard work, they will live better lives because of it. They motivate me.

The blog is back, I hope

  What started as a way to share news about HPS and what it is like to live with Hermansky-Pudlak Syndrome has fallen apart badly! There are a lot of reasons for this. Some are related to health. Some are related to time. And some are related to mental health. Finally, the last obstacle was technical. I lost access to my blog. Every time I started to work on regaining access, something interrupted the process and I’d have to start all over again. Before you say it, I know. A blog is so old school. Haven’t you heard of a vlog Heather? Or maybe TikTok? I know my limits. I have a great face for radio. I’m not particularly eager to film myself. When I do, I feel I need to spend extra time putting on makeup or fixing my hair. Yet, often when I have the time to do something like this, it is early in the morning or late at night. I don’t want to “get ready.” I’m having a hard enough time squeezing this in without staging myself. Grin. I’m trying to start with small goals. Right now, I’m h