Skip to main content

Hundred People Search Summary and Update

The 21st annual HPS Conference is behind us, which means it's time to start the year's Hundred People Search (H.P.S.) over again. For the last year, we added a total of 66 new HPSers to the patient registry. That fell short of our record by five. 

This might not sound like a lot, but for a disease many of us were told we couldn't have because it is so rare, it is. Also, consider that this is more than one family diagnosed a week. Gladly, we help more families than this get tested every week. Many more test negative and can go away happily knowing HPS is something they need not worry about. 

Let me be clear. I would never want anyone to have HPS. It's my hope that we find the cure and none of us have to have it. However, having HPS and not knowing it can be so dangerous! Accurate diagnosis is so important. 

That is why we issue the Hundred People Search challenge every year. It's up to us - the membership of the HPS Network - to be the voice to help others get an accurate diagnosis. 

One step more than that, it is very important that people with HPS around the world be on the Network's patient registry. Not everyone can be seen at NIH. Because NIH is a government institution, they can not be seen to solicit research participation by patients. There are all these rules that govern what they can and cannot do. Thus, it is up to us. 

Being on the registry means that when there are important developments (like say someday a treatment) we can find you and let you know. 

Thus, it is important to not only be on the registry, but to keep those contact details up to date! 

Comments

Popular posts from this blog

Ratner's Cheesecake

Here's another recipe from Toby! Thanks Toby......and I'll get the others posted soon! Ratner's Cheesecake and plain cookies Ratner's was a Jewish dairy restaurant in the lower East Side of Manhattan. This recipe, from my disintegrating, no longer in print Ratner's cookbook, is the closest I've ever gotten to reproducing the rich, heavy cheesecake my mother made when I was a kid. It's worth the time it takes to prepare and every last calorie. Dough Can be prepared in advance. Makes enough for two cakes. Can be frozen or used to make cookies – see recipe below. 1 cup sugar 1 teaspoon vanilla extract 1 cup shortening 1 teaspoon lemon extract 1 cup butter 2 eggs 3 cups sifted cake flour ½ teaspoon salt 2 cups all purpose flour 1 teaspoon baking powder 1. In a bowl, combine all ingredients with hands. Refrigerate 3 -4 hours, or preferably overnight. Filling (for

The next generation with Hermansky-Pudlak Syndrome

I'm so behind on posting about the trip to Puerto Rico. Since the episode of Mystery Diagnosis on Hermansky-Pudlak Syndrome ran right after we got home, it's been a little busy. These, however, are my favorite pictures from Puerto Rico. I know, not pretty senery etc - but these little guys and gals inspire me. They are the next generation of folks with HPS, and if we keep up the hard work, they will live better lives because of it. They motivate me.

Some good news about Pirfenidone

Below is a press release from Intermune, the company that makes Pirfenidone. They have essentially reviewed the various clinical trials going on, and decided that Pirfenidone is safe and well tolerated. That would pretty much go along with what we've observed in the HPS community as well. We have a few folks that have been on the drug since the late 90s and continue to do well. Of course, as a journalist, I do have to say consider the source - but at the same time, as someone in a Pirfenidone trial, it's good to know. Results of Comprehensive Safety Analysis of pirfenidone In IPF Patients Presented At European Respiratory Meeting - Analysis shows safety and tolerability of pirfenidone across four clinical trials - VIENNA, Sept. 14 /PRNewswire-FirstCall/ -- InterMune, Inc. (Nasdaq: ITMN ) today announced that the results of a comprehensive review of safety data from four clinical studies were presented at the 2009 European Respiratory Society Annual Congress in Vienna, Austria