Skip to main content

Quick health update

It's been a long time since I've written a health update. Mom is on her way to pick me up and I've got tons to do, so shouldn't be doing this either - but oh well. I haven't posted much about my health lately because there hasn't been much new to say. It isn't that everything is fine, but more that it's the same old stuff. 


Friday I had my first appointment with my new local pulmo. doc. It was a great appointment and I like him. I feel like he  "gets it" which, when you have something rare, isn't always a feeling you go away with on the first appointment. 


I was very lucky to meet him at the American Thoracic Society meeting. Actually, I'm surprised we didn't scare him away! He came to the booth looking for information about HPS because he knew he had a new patient coming in with it. As I'd just made the appointment, I took a chance and asked him if he was from KUMed. He said he was, and I introduced myself as his new patient. 


He got lots of info about HPS, hugs from Donna and the twins and someone from the Coalition for Pulmonary Fibrosis we were chatting with as he came up. He got the story of my life from Donna - giggle. And still, he's taking me on! You've got to give the guy kudos! 


My pulmonary function tests were all pretty much the same as before, but the DLCO is still a bit low. 


One of this doc's areas of specialty is pre and post lung transplant care. We had a talk about when that "day" arrives. 


He seems a little concerned that I might be developing pulmonary hypertension and so I'm having some tests done on my heart. It isn't so much that I didn't already know I was at high risk for developing this complication, but the suggestion did rattle me a bit. The other HPS'ers that I've known with this complication developed it when they were much closer to needing a transplant than I perceive myself to be. Still, if it is there, it's still quite mild and hopefully can be treated (although there isn't really a cure for it - story of my life!) 



Comments

Popular posts from this blog

Ratner's Cheesecake

Here's another recipe from Toby! Thanks Toby......and I'll get the others posted soon! Ratner's Cheesecake and plain cookies Ratner's was a Jewish dairy restaurant in the lower East Side of Manhattan. This recipe, from my disintegrating, no longer in print Ratner's cookbook, is the closest I've ever gotten to reproducing the rich, heavy cheesecake my mother made when I was a kid. It's worth the time it takes to prepare and every last calorie. Dough Can be prepared in advance. Makes enough for two cakes. Can be frozen or used to make cookies – see recipe below. 1 cup sugar 1 teaspoon vanilla extract 1 cup shortening 1 teaspoon lemon extract 1 cup butter 2 eggs 3 cups sifted cake flour ½ teaspoon salt 2 cups all purpose flour 1 teaspoon baking powder 1. In a bowl, combine all ingredients with hands. Refrigerate 3 -4 hours, or preferably overnight. Filling (for

The next generation with Hermansky-Pudlak Syndrome

I'm so behind on posting about the trip to Puerto Rico. Since the episode of Mystery Diagnosis on Hermansky-Pudlak Syndrome ran right after we got home, it's been a little busy. These, however, are my favorite pictures from Puerto Rico. I know, not pretty senery etc - but these little guys and gals inspire me. They are the next generation of folks with HPS, and if we keep up the hard work, they will live better lives because of it. They motivate me.

Some good news about Pirfenidone

Below is a press release from Intermune, the company that makes Pirfenidone. They have essentially reviewed the various clinical trials going on, and decided that Pirfenidone is safe and well tolerated. That would pretty much go along with what we've observed in the HPS community as well. We have a few folks that have been on the drug since the late 90s and continue to do well. Of course, as a journalist, I do have to say consider the source - but at the same time, as someone in a Pirfenidone trial, it's good to know. Results of Comprehensive Safety Analysis of pirfenidone In IPF Patients Presented At European Respiratory Meeting - Analysis shows safety and tolerability of pirfenidone across four clinical trials - VIENNA, Sept. 14 /PRNewswire-FirstCall/ -- InterMune, Inc. (Nasdaq: ITMN ) today announced that the results of a comprehensive review of safety data from four clinical studies were presented at the 2009 European Respiratory Society Annual Congress in Vienna, Austria